Kartagener syndrome (KS), a rare genetic disorder, is characterized by the triad of situs inversus, chronic sinusitis, and bronchiectasis. It often presents unique challenges in clinical management, particularly when the bronchiectasis is complicated by massive hemoptysis. We present a case of a 32-year-old male with KS who presented to the emergency department with massive hemoptysis. Despite initial resuscitative measures, the patient's condition remained critical. Following a multidisciplinary approach, bronchial artery embolization (BAE) was performed, achieving successful hemostasis. This case highlights the effectiveness of BAE as a life-saving intervention in managing massive hemoptysis in patients with KS.
Castillo M, Freire E, Romero VI. Primary ciliary dyskinesia diagnosis and management and its implications in America: a mini review. Front Pediatr 2023;(11):1091–1173. DOI: 10.3389/fped.2023.1091173
Anand R, Rowther ML, Rashmi ML, et al. Case series of Kartagener syndrome: a rare genetic disorder with variable pulmonary presentation. Indian J Respir Care 2024;13(2):136–139. DOI: 10.5005/jp-journals-11010-1107
Ibrahim WH. Massive hemoptysis: the definition should be revised. Eur Respir J 2008;32(4):1131-1132. DOI: 10.1183/09031936.00080108
Fishman AP, Elias JA, Fishman JA, et al. Hemoptysis and its management in bronchiectasis patients: role of bronchial artery embolization (BAE). In: Fishman's Pulmonary Diseases and Disorders. 5th ed. New York: McGraw-Hill Education; 2020. pp. 897–905.
Shera TA, Bhalla AS, Naranje P, et al. Role of computed tomography angiography in the evaluation of hemoptysis in children: Decoding the abnormal vessels. Indian J Med Res 2022;155(3,4):356–363. DOI: 10.4103/ijmr.IJMR_3271_20
Ewen R, Pink I, Sutharsan S, et al. Primary Ciliary Dyskinesia in Adult Bronchiectasis: Data from the German Bronchiectasis Registry PROGNOSIS. Chest 2024;166(5):938–950. DOI: 10.1016/j.chest.2024.05.023
Radchenko C, Alraiyes AH, Shojaee S. A systematic approach to the management of massive hemoptysis. J Thorac Dis 2017;9(10):S1069–S1086. DOI: 10.21037/jtd.2017.06.41