Background: Ebstein's anomaly is a rare congenital cardiac defect causing atrialization of the right ventricle (RV) and has a wide spectrum of clinical presentation depending on the severity of the lesion.
Case description: A 28-year-old G2P1L1 female at 36 weeks of gestation was evaluated for acute febrile illness and diagnosed with H1N1 influenza. During the clinical examination, a pansystolic murmur was heard, prompting a cardiac evaluation. A two-dimensional (2D) echocardiogram was performed and suggested Ebstein's anomaly with atrialized RV, which had remained undiagnosed during both her pregnancies. She had a further uneventful pregnancy and an uncomplicated delivery by cesarean section of a healthy child.
Conclusion: Ebstein's anomaly has varying presentations and may remain asymptomatic depending on the severity of the lesion. Outcomes in pregnancy are generally favorable.
Clinical significance: A thorough cardiac evaluation is important in antenatal checkups for early detection of any cardiac anomaly and its appropriate management to reduce risk to both mother and fetus.
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